Achondroplasia
Phase 1: Consultation and Initial Evaluation
You will be met by the General Director of the Ilizarov Centre for Traumatology and Orthopaedics as well as your appointed orthopaedic surgeon. After a rudimentary physical evaluation and discussion of your desired height goal, the meeting will proceed regarding our recommended best course of treatment according to your requests. All aspects of the Ilizarov lengthening procedure will be conveyed to you and translators will be present during the meeting for the aid of communication and clarification.


Phase 2: Preparation and Preoperative Visit
It is required that a comprehensive physical examination be performed for each patient before surgery. These are completed at the Ilizarov Centre by our range of specialist physicians. Depending on your age and health status, assessments such as blood tests, electrocardiography, and radiography of the tibias or femurs are required prior to the surgery. As part of the preoperative visit, informed consent will be obtained and questions regarding the surgery will be answered. At this point your surgeon will determine the appropriate sized frames which will support you during the lengthening and consolidation process. You will also be scheduled a meeting with your anethesiologist before undergoing your surgery to discuss any allergies or specific requirements that you may have.


Phase 3: Surgery For lengthening, a corticotomy on the appropriate bone is performed through a small incision to minimise injury of surrounding tissue. The external fixator Ilizarov frames are then attached to the bone using pins that pass through the tibias/femurs depending on which bone is to be lengthened. After surgery, patients remain in the hospital for the entire duration of their treatment so as to ensure that the risk of complications are minimised. Immediately after surgery you will receive constant monitoring by our team of qualified nurses and daily post-operative visits by your doctor. Our physical therapists initiate rehabilitation sessions a few days after surgery and patients are taught to walk using crutches ensuring that they remain physically active during the lengthening and consolidation phases.


Phase 4: Distraction
Phase Lengthening usually begins a few days or a week after surgery. At the Ilizarov Centre, this is done either manually or by means of motors. The manual turns are performed by the Centre's nurses and the motors run automatically however can be turned on or shut down manually. As bone is a living substance, when its ends are gradually distracted, new bone grows between the two ends. The lengthening rate is usually 1 mm per day but may be slower or faster depending on the tolerance of the bone and soft tissues to the distraction process. Most patients experience little pain during the day. Aching or difficulty sleeping at night is not unusual but is well controlled with medications as required. This varies between patients according to individual pain tolerance and the type of treatment being performed. Physical therapy is required on an inpatient basis in all cases during the distraction phase. These sessions are designed to stretch muscles assisting their growth and to maintain joint flexibility. In most cases, we allow partial or complete weight bearing as this process stimulates new bone to grow - much in the same way stretching stimulates muscles and other soft tissues to grow. During the distraction phase, you will be examined and x-rays will be obtained every two weeks to evaluate bone growth, nerve and muscle function, and pin sites. The distraction rate will be constantly adjusted by your doctor according to the strength of your regeneration and your body's tolerance of the lengthening process. A feature unique to the Ilizarov method is that correction to the lengthening bone can be performed due to the frames completely surrounding it in a 360° fashion. Corrections are essential during the distraction process as it ensures that both bones ultimately are of equal length as well as shape. This results in the optimum desired aesthetic effect being achieved for our patients.


Achondroplasia
Achondroplasia



Phase 5: Consolidation Phase
After the desired lengthening has been achieved, adjustments and correction with the Ilizarov frame cease. Newly regenerated bone is weak at this stage and would be unable to resist compression or fractures without the continued support of the external fixation device. Thus, the external frame remains in place until the end of the consolidation phase. The average total external treatment time is 1 month per centimeter (therefore achieving 5cm in height should take approximately 5 months to complete including the distraction and fixation phases). Bone regeneration and the levels of calcium present is assessed according to patient x-rays.


Phase 6: Removal of the External Frame
Once sufficient calcium is identified throughout the regeneration region, the apparatus is then removed through a brief non-surgical process causing very little pain or discomfort for the patient. After removal, patients are required to wear a cast for one month as a form of additional protection of the newly generated bone.


Phase 7: Rehabilitation Phase
At our Centre it is standard for patients to walk and perform normal tasks and functions after their casts are removed. Our specialist physiotherapists will work with patients through a comprehensive rehabilitation program to restore all normal leg and foot functions. When deemed appropriate, assessments by your doctor and the Centre's general director will be conducted to ensure that functionality is restored prior to patients being released from our Centre.



Achondroplasia
Patient R., age 22, underwent lengthening of both tibias by Ilizarov method of bilocal distractive osteosynthesis. Lengthening 7 cm.
Dwarfs


Dwarfs
Patient, age 34, underwent lengthening and axial correction of both tibias by Ilizarov method of bilocal distractive osteosynthesis. Lengthening 5 cm.
Height Increase Othopaedics


Height Increase Othopaedics
Patient, age 25, underwent lengthening of tibias and subsequently femurs by Ilizarov method of bilocal distractive osteosynthesis. Lengthening 14 cm.




Distraction Pain
Pain during the distraction process is a standard consequence of any lengthening technique. Most patients do not experience extensive pain in the day however difficulty attaining adequate amounts of sleep is a common occurrence during the distraction phase. These are controlled with the aid of medications according to the individual requirements and tolerance of each patient. Pain encountered during the distraction process is due to the accompanying lengthening of soft tissues such as muscles and tendons. Thus, once fixation has been achieved all pain encountered from distraction dissipates within a few days and is no longer an issue during consolidation.

Soft Tissue Contraction
While lengthening bone, it is necessary to practice physical therapy to ensure that tendons and other soft tissues are expanding proportionally. However, contraction often occurs as a consequence of muscle weakening and patient inactivity during the distraction process. This prevents the patient from completely straightening their leg and occurs in varying degrees depending on the severity of each circumstance. The condition however is temporary as contracted tissues such as muscles and tendons are soft and flexible in structure. It is therefore invariably rectified during the consolidation phase through implementing the Centre's appropriate physiotherapy exercises and stretches. Due to our 50 yrs experience in treating thousands of height increase cases, the Centre possesses one of the world's most developed exercise programs specifically devised to address tissue contracture. And although physical therapy may appear to be a trivial issue, it is in fact the sole determining factor which renders a height increase procedure as either a success or a failure.

Numbness
Many patients experience numbness in limited areas around the feet following surgery and while distracting. This is caused by post operative swelling thus inhibiting proper nerve function during lengthening. Sensation is gradually restored during fixation as nerve irritation and swelling has ceased during this phase with patients recovering their full sensations.

Scarring
Scarring is a prevalent issue when lengthening with the Ilizarov method. As metal pins are utilised to support the bone, scars form on the skin due to the stretching incurred while distracting. The Centre offers scar treatment additional to height increase in order to assist with the cosmetic aspect of this procedure. Results are aesthetically extremely effective and scar removal has now become a very common procedure being available in most patients' local areas. Patients are therefore presented with the option to treat their scars at the Centre or when they return home from their height increase procedure.



Since the development of the Ilizarov external fixator frames in 1951 a number of other height increase methods have arisen in smaller clinics in countries such as France and Germany. The majority of these alternative methods consist of inserting and securing internal lengthening devices to the inner bone cavity. These procedures are designed to reduce scarring to the patient's limbs and provide more convenience during lengthening and fixation however these methods are also accompanied by a number of drawbacks. The most common devices include those of Albizzia, Bliskunov and Fitbone and their practical application is restricted exclusively to the femur. The option of lengthening the tibia is not provided by internal methods as the tibia's internal cavity is too small to accommodate a functional lengthening device.

Internal devices, as they are situated within the patient's bone, offer less stability and less control during the lengthening process. Many difficulties occur during distraction in regards to the performance and function of internal devices and these cannot be rectified without the necessity of additional surgery. These methods are therefore considered to still exist within their experimental state due to their low success rate with a number of patients having been found to depend on crutches one to two years after lengthening. This also accounts for the reason why internal methods are not approved by the FDA.

A significant drawback to these alternative devices is that corrections to the shape of the leg may not be performed to assist in the aesthetic aspect of lengthening. Thus distraction and lengthening can be achieved without improvements to the shape and therefore functionality of the limb - a factor which is not an issue with the Ilizaorv frame.

Another associated issue of internal devices is the development of serious secondary complications (such as inadequate lengthening of the surrounding soft tissue). This method of lengthening performed on the femur poses a higher risk due to its close proximity to the spinal column and cord. Contraction often occurs in the backs of internal device patients causing permanent damage to their stature. Therefore, in all height increase cases it is primarily recommended that lengthening be performed on the tibia as opposed to the femur for security reasons as well as aesthetic reasons. Additionally, as patients are considered more independent with the internal apparatus, lengthening is performed on an outpatient basis thus resulting in a higher complication rate from lack of supervision and the appropriate physical therapy pivotal to the success of any height increase procedure.